地中海贫血患者的听损伤

江珊;陈平;

1:广西医科大学第一附属医院耳鼻咽喉头颈外科

摘要
<正>地中海贫血(简称地贫)又称作"海洋性贫血"或"珠蛋白生成障碍性贫血",主要是珠蛋白基因缺失或突变导致珠蛋白肽链合成障碍,引起一种或几种肽链合成受到部分或完全抑制,使构成血红蛋白的各肽链比例失衡所致的遗传性溶血性贫血;因受累珠蛋白基因的不同可分为ɑ与β地中海贫血,我国以β地中海贫血较为多见[1]。根据其临床表现又可分为轻型、中间型和重型,轻型患者多无症状或症状较轻,通常可不需治疗;重型患儿多于出生后半年到
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江珊;陈平;
参考文献

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江珊陈平