PJVK基因与听神经病

张秋静;王秋菊;

1:解放军总医院耳鼻咽喉-头颈外科解放军耳鼻咽喉科研究所

摘要
<正>听神经病(auditory neuropathy,AN)是听神经功能异常而外毛细胞功能正常的一种听觉障碍性疾病,系听觉信息传输处理过程的异常[1]。临床表现[26]为以言语辨别能力下降为主的听力损失,言语识别率差,与纯音听阈不成比例;听力损失可为轻度、中度到重度;耳声发射多正常或轻度改变,听性脑干反应严重异常,声刺激镫骨肌反射消失或阈值升高。1996年Starr等首次将这组症候群命名为"听神经病"[7]。
关键词
基金项目(Foundation):
国家自然基金重点及面上项目(30830104&30771203);; 北京市自然科学基金重大项目(7070002);; 国家"十一五"科技支撑计划(2007BAI18B12)联合资助
作者
张秋静;王秋菊;
参考文献

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张秋静王秋菊