大前庭水管综合征患者的听力学特点

Audiological Features of Large Vestibular Aqueduct Syndrome

刘辉;董玉云;莫玲燕;孙玉兰;陈雪静;

1:首都医科大学附属北京同仁医院耳鼻咽喉-头颈外科

2:首都医科大学附属北京同仁医院耳鼻咽喉-头颈外科

3:北京市耳鼻咽喉科研究所

4:首都医科大学附属北京同仁医院耳鼻咽喉-头颈外科

摘要
目的探讨大前庭水管综合征(large vestibular aqueduct syndrome,LVAS)患者的听力学特点。方法对19例(38耳)LVAS患者进行了纯音听阈测试、盖莱氏试验、声导抗测试及颞骨高分辨CT检查。结果19例(38耳)患者CT检查均为单纯前庭水管扩大。纯音测听34耳为混合性聋,低频骨气导差较大,中高频骨气导差较小。28耳鼓室导抗图均为A型,20耳可引出声反射,声反射阈与听阈之差平均为28 dB HL。28耳进行了共振频率测试,中耳共振频率为652±175 Hz,较正常耳低(P<0.01)。18耳进行了盖莱氏试验,均为阳性。结论LVAS患者可表现为感音神经性聋,也可表现为混合性聋。混合性聋患者在听力较好时可引出声反射,是该病的特征性表现。另外,该病呈混合性聋时,还可能意味着病变的可逆性。
关键词
大前庭水管综合征;听力损失;混合性;听力测试
基金项目(Foundation):
作者
刘辉;董玉云;莫玲燕;孙玉兰;陈雪静;
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