双侧蜗神经发育不良患儿人工耳蜗植入后听觉言语康复效果及影响因素分析
Analysis of the effect and influencing factors of auditory and speech rehabilitation after cochlear implantation in children with bilateral cochlear deficiency
张晓;杨扬;刘薇;刘瀚迪;陈敏;马宁;刘冰;邵剑波;刘海红;郑军;张杰
1:国家儿童医学中心
2:首都医科大学附属北京儿童医院耳鼻咽喉头颈外科
3:儿童耳鼻咽喉头颈外科疾病北京市重点实验室
4:首都医科大学附属北京同仁医院耳鼻咽喉头颈外科





[1] PENG K A,KUAN E C,HAGAN S,et al.Cochlear nerve aplasia and hypoplasia:predictors of cochlear implant success[J].Otolaryngol Head Neck Surg,2017,157(3):392-400.
[2] JAMES A L,DIXON P R,HARRISON R V.Cochlear nerve aplasia with detectable olivocochlear efferent function:adistinct presentation of auditory neuropathy spectrum disorder[J].Audiol Neurootol,2018,23(1):39-47.
[3] CHIOSSO J S C,HYPPOLITO M A.Effects of residual hearing on cochlear implant outcomes in children:a systematic-review[J].Int J Pediatr Otorhinolaryngol,2017,100:119-127.
[4] 樊小勤,林颖,任林,等.蜗神经发育不良患者的听力学特征分析[J].听力学及言语疾病杂志,2020,28(1):15-18.
[5] KARI E,GILLARD D M,CHUANG N,et al.Can imaging predict hearing outcomes in children with cochleovestibular nerve abnormalities?[J].Laryngoscope,2022,132(Suppl 8):S1-S15.
[6] VESSEUR A,FREE R,SNELS C,et al.Hearing restoration in cochlear nerve deficiency:the choice between cochlear implant or auditory brainstem implant,a meta-analysis[J].Otol Neurotol,2018,39(4):428-437.
[7] KONO T.Computed tomographic features of the bony canal of the cochlear nerve in pediatric patients with unilateral sensorineural hearing loss[J].Radiation Medicine-Medical Imaging and Radiation Oncology,2008,26(3):115-119.
[8] BIRMAN C S,POWELL H R F,GIBSON W P R,et al.Cochlear implant outcomes in cochlea nerve aplasia and hypoplasia[J].Otology and Neurotology,2016,37(5):438-445.
[9] 张道行.蜗神经孔狭窄和闭锁的诊断与人工耳蜗植入术后效果[J].临床耳鼻咽喉头颈外科杂志,2014,28(15):1101-1104.
[10] 王丽燕,申敏,梁巍,等.扩展版CAP问卷的中文版开发及其信效度研究[J].中国听力语言康复科学杂志,2020,18(5):367-369.
[11] 王宇,潘滔,米思,等.中文版言语可懂度分级标准的建立及其信度检验[J].听力学及言语疾病杂志,2013,21(5):465-468.
[12] 赵天峰,陈俊,任寸寸,等.复杂内耳畸形患儿人工耳蜗植入术后疗效分析[J].听力学及言语疾病杂志,2021,29(5):504-508.
[13] 莫玲燕,燕飞,刘辉,等.小儿蜗神经发育不良[J].听力学及言语疾病杂志,2011,19(5):402-405.
[14] 钟梅芳,洪晓纯,李楚凌.蜗神经发育不良儿童的临床特征分析[J].听力学及言语疾病杂志,2020,28(3):267-272.
[15] WEI X M,LI Y X,CHEN B,et al.Predicting auditory outcomes from radiological imaging in cochlear implant patients with cochlear nerve deficiency[J].Otology Neurotology,2017,38(5):685-693.
[16] ARUMUGAM S V,NAIR G,PARAMASIVAN V K,et al.A study of outcome of pediatric cochlear implantation in patients with cochleovestibular nerve deficiency[J].J Int Adv Otol,2020,16(2):147-152.
[17] OTHMAN I A,ABDULLAH A,SEE G B,et al.Auditory performance in early implanted children with cochleovestibular malformation and cochlear nerve deficiency[J].J Int Adv Otol,2020,16(3):297-302.
[18] KUTZ J W,LEE K H,ISAACAON B,et al.Cochlear implantationin children with cochlear nerve absence or deficiency[J].Otol Neurotol,2011,32(6):956-961.
[19] THIERRY M,MARKIAN P,ROBERT C,et al.Cochlear nerve deficiency and brain abnormalities in pediatric patients[J].Otology Neurotology,2017,38(3):429-440.
[20] 刘军.人工耳蜗植入术前耳蜗神经及后通路功能评估[J].中国听力语言康复科学杂志,2023,21(5):449-455.
[21] CHIEKO E,SHUJIRO M,KIMITAKA K.EABR measurements during cochlear implantation in one-year-old,infant,child,adult,and elderly patients[J].Acta Oto-laryngologica,2021,141(1):78-82.
[22] 苏金霏,张道行.蜗神经管狭窄患者人工耳蜗植入术后听觉康复效果分析[J].听力学及言语疾病杂志,2016,24(4):386-390.