1 Goravalingappa R,Han JC,Mangiardi J,et al.Congenital auricular malformations:description of anomalies and syndromes[J].Facial Plast Surg,2015,31:567．

2 Global estimates on prevalence of hearing loss.Geneva:World Health Organization;2018.Available from:http：//www.who.int/pbd/deafness/estimates/en/．

3 Danhauer JL,Johnson CE,Mixon M.Does the evidence support use of the Baha implant system(Baha)in patients with congenital unilateral aural atresia[J]?J Am Acad Audiol,2010,21:274．

4王青森，张淼，邹艺辉．先天性中外耳畸形患者纯音听力特点分析[J]．中华耳科学杂志，2018,16:12．

5 Priwin C,J9nsson R,Magnusson L,et al.Audiological evaluation and self-assessed hearing problems in subjects with single-sided congenital external ear malformations and associated conductive hearing loss[J].International Audiology,2007,46:162．

6 van H9vell Tot Westerflier C,van Heteren J,Breugem CC,et al.Impact of unilateral congenital aural atresia on academic performance:a systematic review[J].Int J Pediatr Otorhinolaryngol,2018,114:175．

7 Kesser BW,Krook K,Gray LC.Impact of unilateral conductive hearing loss due to aural atresia on academic performance in children[J].Laryngoscope,2013,123:2270．

8 Fischer C,Lieu J.Unilateral hearing loss is associated with a negative effect on language scores in adolescents[J].Int J Pediatr Otorhinolaryngol,2014,78:1611．

9 DieudonnéB,Francart T.Head shadow enhancement with low-frequency beamforming improves sound localization and speech perception for simulated bimodal listeners[J].Hear Res,2018,363:78．

10 Dincer D'Alessandro H,Sennaroˇglu G,Yücel E,et al.Binaural squelch and head shadow effects in children with unilateral cochlear implants and contralateral hearing aids[J].Acta Otorhinolaryngol Ital,2015,35:343．

11 Kesser BW,Cole ED,Gray LC.Emergence of binaural summation after surgical correction of unilateral congenital aural atresia[J].Otol Neurotol,2016,37:499．

12 Vyskocil E,Liepins R,Kaider A,et al.Sound localization in patients with congenital unilateral conductive hearing loss with a transcutaneous bone conduction implant[J].Otol Neurotol,2017,38:318．

13刘强，夏寅．声源定位及BAHA对声源定位影响的研究进展[J]．听力学及言语疾病杂志，2016,24:301．

14 De la Cruz A,Teufert KB.Congenital aural atresia surgery:long-term results[J].Otolaryngol Head Neck Surg,2003,129:121．

15 Jahrsdoerfer RA,Yeakley JW,Aguilar EA,et al.Grading system for the selection of patients with congenital aural atresia[J].Am J Otol,1992,13:6．

16 Li C,Zhang T,Fu Y,et al.Congenital aural atresia and stenosis:surgery strategies and long-term results[J].Int JAudiol,2014,53:476．

17赵守琴，韩德民，戴海江，等．伴皮肤窦道的先天性外耳道狭窄及胆脂瘤的诊断与治疗[J]．中华耳鼻咽喉头颈外科杂志，2009,44:118．

18 Lo JF,Tsang WS,Yu JY,et al.Contemporary hearing rehabilitation options in patients with aural atresia[J].Biomed Res Int,2014,2014:761579．

19 Sprinzl G,Lenarz T,Ernst A,et al.First European multicenter results with a new transcutaneous bone conduction hearing implant system:short-term safety and efficacy[J].Otol Neurotol,2013,34:1076．

20 Roman S,Nicollas R,Triglia JM.Practice guidelines for bone-anchored hearing aids in children[J].Eur Ann Otorhinolaryngol Head Neck Dis,2011,128:253．

21 Yu JK,Wong LL,Tsang WS,et al.A tutorial on implantable hearing amplification options for adults with unilateral microtia and atresia[J].Biomed Res Int,2014,2014:1．

22 Heywood RL,Patel PM,Jonathan DA.Comparison of hearing thresholds obtained with Baha preoperative assessment tools and those obtained with the osseointegrated implant[J].Ear Nose Throat J,2011,90:E21．

23 Kunst SJ,Hol MK,Mylanus EA,et al.Subjective benefit after BAHA system application in patients with congenital unilateral conductive hearing impairment[J].Otol Neurotol,2008,29:353．

24 Neumann K,Thomas JP,Voelter C,et al.A new adhesive bone conduction hearing system effectively treats conductive hearing loss in children[J].Int J Pediatr Otorhinolaryngol,2019,122:117．

25 Leinung M,Zaretsky E,Lange BP,et al.Vibrant Soundbridgein preschool children with unilateral aural atresia:acceptance and benefit[J].Eur Arch Otorhinolaryngol,2017,274:159．

26王丹妮，赵守琴，李轶，等．先天性前庭窗闭锁的圆窗模式振动声桥植入（附9例报告）[J]．临床耳鼻咽喉头颈外科杂志，2017,31:588．

27 Mosnier I,Sterkers O,Bouccara D,et al.Benefit of the vibrant soundbridge device in patients implanted for 5to 8years[J].Ear Hear,2008,29:281．

28 Bruchhage KL,Leichtle A,Sch9nweiler R,et al.Systematic review to evaluate the safety,efficacy and economical outcomes of the vibrant soundbridge for the treatment of sensorineural hearing loss[J].Eur Arch Otorhinolaryngol,2017,274:1797．

29 Zhao S,Wang D,Han D,et al.Integrated protocol of auricle reconstruction combined with hearing reconstruction[J].Acta Otolaryngol,2012,132:829．

30 Wang D,Zhao S,Zhang Q,et al.Vibrant sound bridge combined with auricle reconstruction for bilateral congenital aural atresia[J].Int J Pediatr Otorhinolaryngol,2016,86:240．

31 Wang Y,Xing W,Liu T,et al.Simultaneous auricular reconstruction combined with bone bridge implantation-optimal surgical techniques in bilateral microtia with severe hearing impairment[J].Int J Pediatr Otorhinolaryngol,2018,113:82．

32赵守琴．先天性中耳畸形的诊断与治疗[J]．听力学及言语疾病杂志，2016,24:113．

33 Kunst SJ,Leijendeckers JM,Mylanus EA,et al.Bone-anchored hearing aid system application for unilateral congenital conductive hearing impairment:audiometric results[J].Otol Neurotol,2008,29:2．

34 Byun H,Moon IJ,Woo SY,et al.Objective and subjective improvement of hearing in noise after surgical correction of unilateral congenital aural atresia in pediatric patients:aprospective study using the hearing in noise test,the soundspatial-quality questionnaire,and the glasgow benefit inventory[J].Ear Hear,2015,36:e183．

35 Moon IJ,Byun H,Jin SH,et al.Sound localization performance improves after canaloplasty in unilateral congenital aural atresia patients[J].Otol Neurotol,2014,35:639．

36 Pfiffner F,Kompis M,Stieger C.Bone-anchored hearing aids:correlation between pure-tone thresholds and outcome in three user groups[J].Otol Neurotol,2009,30:884．

37 Van de Heyning P,Távora-Vieira D,Mertens G,et al.Towards a unified testing framework for single-sided deafness studies:a consensus paper[J].Audiol Neurootol,2016,21:391．

38 Gray L,Kesser B,Cole E.Understanding speech in noise after correction of congenital unilateral aural atresia:effects of age in the emergence of binaural squelch but not in use of head-shadow[J].Int J Pediatr Otorhinolaryngol,2009,73:1281．

39 Priwin C,J9nsson R,Hultcrantz M,et al.BAHA in children and adolescents with unilateral or bilateral conductive hearing loss:a study of outcome[J].Int J Pediatr Otorhinolaryngol,2007,71:135．

40 Frenzel H,Hanke F,Beltrame M,et al.Application of the vibrant soundbridge to unilateral osseous atresia cases[J].Laryngoscope,2009,119:67．

41 Vogt K,Frenzel H,Ausili SA,et al.Improved directional hearing of children with congenital unilateral conductive hearing loss implanted with an active bone-conduction implant or an active middle ear implant[J].Hear Res,2018,370:238．

42 Nelissen RC,Agterberg MJ,Hol MK,et al.Three-year experience with the Sophono in children with congenital conductive unilateral hearing loss:tolerability,audiometry,and sound localization compared to a bone-anchored hearing aid[J].Eur Arch Otorhinolaryngol,2016,273:3149．

43 Agterberg MJ,Frenzel H,Wollenberg B,et al.Amplification options in unilateral aural atresia:an active middle ear implant or a bone conduction device[J]?Otol Neurotol,2014,35:129．

44 Irving S,Moore DR.Training sound localization in normal hearing listeners with and without a unilateral ear plug[J].Hear Res,2011,280:100．

45 Gatehouse S,Noble W.The speech,spatial and qualities of hearing scale(SSQ)[J].Int J Audiol,2004,43:85．

46 Robinson K,Gatehouse S,Browning GG.Measuring patient benefit from otorhinolaryngological surgery and therapy[J].Ann Otol Rhinol Laryngol,1996,105:415．

47 Kubba H,Swan IR,Gatehouse S.The Glasgow children's benefit inventory:a new instrument for assessing health-related benefit after an intervention[J].Ann Otol Rhinol Laryngol,2004,113:980．

48 American Academy of Audiology.Clinical Practice Guidelines on Pediatric Amplification,2013.www.audiology.org/publications-resources/documentlibrary/pediatric-rehabilitation-hearing-aids．

49国家卫生和计划生育委员会新生儿疾病筛查听力诊断治疗组．婴幼儿听力损失诊断与干预指南[J]．中华耳鼻咽喉头颈外科杂志，2018,53:181.